Hypotonic maculopathy secondary to scleral defect in atypical retinochoroidal coloboma



To describe a patient with unilateral hypotonic maculopathy and optic disc edema after spontaneous bulbar perforation of a full-thickness scleral defect.


An 11-year-old girl underwent scleral buckling surgery. Preoperative and postoperative evaluation included optical coherence tomography and high-resolution 3T magnetic resonance imaging.


The scleral defect was covered with Tenon capsule sheaths and a meridional silicone buckle. One year postoperatively, visual acuity and macular and optic disc morphology were completely restored.


Ocular hypotony related to a defect of the sclera forming the roof of a retinochoroidal coloboma is a rare event. Hypotony was a consequence of a defect at the level of an atypical retinochoroidal coloboma where the scleral wall was found to be absent.

Eur J Ophthalmol 2016; 26(6): e161 - e164

Article Type: CASE REPORT



Tito Fiore, Adriana Pellegrino, Marco Lupidi, Alessio Cerquaglia, Fabrizio Giansanti, Carlo Cagini

Article History


Financial support: No financial support was received for this submission.
Conflict of interest: None of the authors has conflict of interest with this submission.
Meeting presentation: The manuscript was presented at STUEMO 2015.

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  • Department of Biomedical and Surgical Sciences, Section of Ophthalmology, University of Perugia, S. Maria della Misericordia Hospital, Perugia - Italy
  • Department of Translational Surgery and Medicine, Eye Clinic, University of Florence, Florence - Italy

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